Volume 13, Issue 1
Original Article / Published: September 2025
DOI: https://www.doi.org/10.57045/jemis/1310925.pp74-79
M. Mihaylova-Hristova, E. Piperkova, L. Chavdarova, M. Zaharinov
Department of Nuclear medicine, USHATO “Prof. Ivan Tzernozemski”, Sofia
Abstract
Desmoplastic small round cell tumor (DSRCT) is an exceptionally rare and highly aggressive primary peritoneal neoplasm predominantly seen in adolescents and young adults. Despite the availability of various treatment modalities, the prognosis remains grim due to the tumor’s aggressive nature and tendency for widespread metastasis. Although imaging of DSRCT is frequently documented using computed tomography (CT), the role of 18F-fluorodeoxyglucose positron emission tomography/computed tomography (18F-FDG PET/CT) in the initial diagnosis, staging, and particularly in the follow-up evaluation, is less explored. We present the case of a 21-year-old male with histologically confirmed desmoplastic small round cell tumor (DSRCT) originating from the right spermatic cord, initially presenting with right scrotal swelling and subsequently found to have extensive intra-abdominal and pelvic metastatic disease on 18F-FDG PET/ CT, highlighting the modality’s crucial role in whole-body staging and therapeutic planning.
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Keywords:
Desmoplastic small round cell tumor, 18F-FDG-PET/CT
How to cite this article:
M. Mihaylova-Hristova, E. Piperkova, L. Chavdarova, M. Zaharinov, Desmoplastic small round cell tumour (dsrct) originating from the right spermatic cord – the role of 18f-fdg pet/ct in the initial staging: a rare case report and literature review. Journal of Endourology and Minimally Invasive Surgery (Bulgaria), 2025; 13(1): 74-79
Corresponding author:
Dr. Maria Mihaylova – Hristova
USHATO “Prof. Ivan Chernozemski“
Clinic of Nuclear Medicine
Sofia,„Plovdivsko pole“ 6 Street
Phone: +359888281463
Email: mariamihaylova347@gmail.com